Status dystonicus, also known as dystonic storm, is a serious and potentially life-threatening disorder which occurs in people who have primary or secondary
dystonia. Symptoms consist of widespread severe muscle contractions. Treatment can be difficult but status dystonicus may respond to
midazolam,
propofol,
baclofen and
bilateralpallidaldeep brain stimulation.[1][2]
References
^Mariotti, P.; Fasano, A.; Contarino, MF.; Della Marca, G.; Piastra, M.; Genovese, O.; Pulitanò, S.; Chiaretti, A.; Bentivoglio, AR. (May 2007). "Management of status dystonicus: our experience and review of the literature". Mov Disord. 22 (7): 963–8.
doi:
10.1002/mds.21471.
PMID17427939.
S2CID40040360.